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Fibrosis pulmonis idiopathica

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Idiopathic pulmonalis Fibrosis (IPF)

signa et causas  

Signa IPF paulatim evolvere et tardius in tempore deteriora facere tendunt. Indicia potest includere: suspirium, assidua tussis arida, languor, appetitus et pondus damnum.

IPF est species pulmonis interstitialis morbus. causatur ex pulmone tela crassa et rigens, et tandem cicatrix intra pulmonem formans. Cicatrix, seu fibrosis, videtur ex cyclo damni et sanationis quae in pulmone occurrunt. Subinde processus sanationis bene laborat et cicatrix texti sistit. Quaenam istarum mutationum inprimis causa sit, ignoratur.

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 exemplum in loco Date➡models】

BLM inductus IPF Model in Rodents 

【Mechanism】Bleomycin (BLM) medicamentum ad varias neoplasmata tractandas usus est. Gravissima adversa effectus BLM est toxicitas pulmonis, quae retexere architecturae pulmonis et amissionem functionis pulmonis, celeriter ducens ad mortem.  

BLM una e late medicamentis adhibitis ad fibrosim pulmonis in animalibus inducendam, ob facultatem pulmonis histologici formam provocandi similem cum patientibus chemotherapyam sustinentibus describit. Praefecti notae sunt inflammatio parenchymatis varius, cellae epithelialis iniuriae cum hyperplasia reciproco, transitus epithelial-mesenchymatis, activatione et differentiatione fibroblastarum ad myofibroblastas, membranam basimentis et epithelii alveolaris iniurias.

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SiO Model2 Adductus Rat IPF

【Mechanism】Silicosis est fatalis occupational morbus pulmonis fibrotici chronici causatus diu terminus expositionis silicae crystallini respirabilis (dioxide pii (SiO 2)) pulvis qui ultimo in airways distalis depositus erat.

In particulis silicae excitandis, T lymphocytes ab antigeno cellulas (APC) praesentantes excitati sunt ut cellulas dendriticas (DC) et macrophages in processu et praesentatione antigenis silicae. Participatio cellularum CD4+T, etiam Th1 et Th2 cellularum, in pathogenesi pulmonis fibrosi a particulis silicis inducta pluribus studiis indicatum est.

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